OXAMIC TRANSCARBAMYLASE OF STREPTOCOCCUS ALLANTOICUS

Mineralization of the recalcitrant oxalic and oxamic

Lanthanide(III) Complexes of Oxamic Acid

The preparation, for the first time, of the deprotonated complexes of oxamic acid with Ce(III), Pr(III), Nd(III), Sm(III), Eu(III), Dy(III), Ho(III ) and Yb(III ) is reported. Properties, analytical results, conductometric measurements, magnetic moments and spectral data (IR and diffuse reflectance spectra) are discussed in terms of possible structural types and the nature of the bonding. Oxami...

Ornithine Transcarbamylase Deficiency

Accumulation of ammonia in body tissues most commonly occurs in hepatic failure. However, it may also result from a specific deficiency of an enzyme of the urea cycle (Fig., 1). Severe hyperammonaemia has been reported with deficiencies of carbamyl phosphate synthetase (Freeman et al., 1964) and ornithine transcarbamylase (Russell et al., 1962; Levin and Russell, 1967). Some increase in blood a...

Antepartum Ornithine Transcarbamylase Deficiency

Ornithine transcarbamylase deficiency (OTCD) is the most common type urea cycle enzyme deficiencies. This syndrome results from a deficiency of the mitochondrial enzyme ornithine transcarbamylase, which catalyzes the conversion of ornithine and carbamoyl phosphate to citrullin. Our case was a 28-year-old female diagnosed with OTCD following neurocognitive deficit during her first pregnancy. Alt...

[Ornithine transcarbamylase deficiency].

Accumulation of ammonia in body tissues most commonly occurs in hepatic failure. However, it may also result from a specific deficiency of an enzyme of the urea cycle (Fig., 1). Severe hyperammonaemia has been reported with deficiencies of carbamyl phosphate synthetase (Freeman et al., 1964) and ornithine transcarbamylase (Russell et al., 1962; Levin and Russell, 1967). Some increase in blood a...